![]() ![]() Effect of conotruncal constriction on aortic-mitral valve continuity in the stage 18, 21 and 24 chick embryo. Dependence of thymus development on derivatives of the neural crest. Neural crest cells contribute to normal aorticopulmonary septation. Complex transposition with interrupted right aortic arch and partial Di George syndrome: successful palliation with combined medical and surgical therapy. Duncan WJ, Tyrrell MJ, Bharadwaj B, Rosenberg AM, Schroeder ML, Bingham WT.Cardiovascular anomalies in DiGeorge syndrome and importance of neural crest as a possible pathogenetic factor. Conley ME, Beckwith JB, Mancer JF, Tenckhoff L.Congenital cardiovascular disease and anomalies of the third and fourth pharyngeal pouch. A rare condition and a cause of bronchial compression. Interruption of the aortic arch with right descending aorta. Pierpont ME, Zollikofer CL, Moller JH, Edwards JE.Cardiovascular malformations in DiGeorge syndrome (congenital absence of hypoplasia of the thymus). Moerman P, Goddeeris P, Lauwerijns J, Van der Hauwaert LG.KLEINERMAN J, YANG WM, HACKEL DB, KAUFMAN N.Interruption of the aortic arch and coarctation of the aorta: pathogenetic relations. Interrupted aortic arch: surgical treatment. Van Praagh R, Bernhard WF, Rosenthal A, Parisi LF, Fyler DC.Links to PubMed are also available for Selected References. Get a printable copy (PDF file) of the complete article (1.2M), or click on a page image below to browse page by page. ![]() Full textįull text is available as a scanned copy of the original print version. If the interruption is associated with a right-sided descending aorta it is highly probable that the patient has DiGeorge syndrome. In patients with an interrupted aortic arch the clinician should be aware of the common association with DiGeorge syndrome. These observations and previous reports indicate that the concurrence of these two rare conditions is more than fortuitous. In a consecutive series of 185 necropsies in infants and children with congenital heart disease there were no cases of interrupted right aortic arch that were not associated with DiGeorge syndrome. Three patients had a bicuspid aortic valve. In two patients there was a doubly committed subarterial ventricular septal defect and in the two other patients there was a perimembranous septal defect. All patients had a mirror image of type B interruption, namely a right aortic arch with reversed branching pattern and an interruption between the right common carotid and right subclavian artery. The clinical and necropsy findings in four cases of interrupted right aortic arch and right descending aorta associated with DiGeorge syndrome (congenital absence or hypoplasia of the thymus and parathyroids) are described. ![]()
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